What is duodenal mucosal lymphangiectasia?
DISCUSSION. Intestinal lymphangiectasia has been well recognized as a disorder characterized by dilated lymphatic vessels of the gastrointestinal tract, especially the small intestine[1-3]. It is a rare condition related to fat malabsorption and protein-losing enteropathy.
What is the treatment for lymphangiectasia?
Treatment of intestinal lymphangiectasia is primarily based on dietary therapy, with high levels of protein and low-fat intake. Many studies reported the effectiveness of surgery and drugs such as octreotide and sirolimus or everolimus for patients who are refractory to dietary therapy [5].
What are the symptoms of lymphangiectasia?
Signs & Symptoms Abdominal pain and/or nausea, vomiting and diarrhea may also be present. Affected individuals may experience fatigue, weight loss, and an inability to gain weight in childhood.
What does lymphangiectasia mean?
Lymphangiectases represent superficial lymphatic dilatation caused by a wide range of scarring processes. Lymphangiectasia occurs as a consequence of lymphatic damage by an external cause, leading to obstruction of local lymphatic drainage. Lymphangiectases are also termed acquired lymphangiomas.
What causes duodenal lymphangiectasia?
This disorder is the result of improperly formed intestinal lymph vessels or blockage of lymph flow from the intestines. Diarrhea and swelling of the legs are the main symptoms. The diagnosis is based on the results of a biopsy.
Can lymphangiectasia be cured?
It should be understood that lymphangiectasia is unlikely to be cured and at best can be managed.
Is lymphangiectasia cancerous?
Lymphangiectasia pose no potential for malignant transformation. Nomenclature has not been consistent 1). Some authors apply the terms acquired lymphangioma and lymphangioma circumscriptum interchangeably.
Is lymphangiectasia fatal?
Lymphangiectasia is rarely cured but can remain in remission for a long time. It can be fatal when unresponsive to treatment.